Synonyms:
a.k.a. dancing eyes dancing feet syndrome
Diagnosis:
This is a clinical syndrome
Clinical features:
- Age: 18 months to 6 years. Can occur in adults
- Opsoclonus: rapid, involuntary, repetitive disorganised congugate eye movements in all directions of gaze. Can be confirmed by oculography: absent intersaccadic interval
Investigations to consider:
- MRI: neuroblastoma
- CT: lung cancer, Hodgkins disease/Hodgkins lymphoma, thyroid cancer
- US thyroid: thyroid cancer
- Mammography: breast cancer
- LP & CSF analysis:
- Brainstem encephalitis
- PCR for whipple’s disease
- Pleocytosis, raised IgG, increased protein
- Other tests for whipple’s disease
- Paraneoplastic antibodies: anti-Ri
Treatment:
Treat the underlying disorder
Steroids