Diagnosis:
Clinical plus EEG
Clinical features:
2-5 years old. Initially GTCS occur, then myoclonic seizures & drop attacks develop. Usual attacks have myoclonic jerks followed by drop attacks. Status epilepticus occurs.
Findings on Investigations:
EEG: Background of 4- to 7-Hz rhythm. Regular or irregular bilaterally synchronous 2- to 3-Hz spike-waves and/or polyspike-waves. Sleep increases he spike-wave
Treatment:
Valproate VPA
Topiramate TPM, clonazepam, clobazam
Ketogenic diet