Diagnosis:
Clinical features of polyneuropathy, mononeuropathy multiplex, biopsy findings of perineuritis and exclusion of secondary causes
Clinical features:
sensory patchy neuropathy, sensorimotor forms exist.
Pathology, nerve biopsy:
Perineurium: inflammatory lymphocytic infiltrate, thickening of perineurium
Exclusion of other causes
Treatment:
Consider corticosteroids