Diagnosis:
Clinical features, plus EEG
Clinical features:
Previous measles infection. Children or young adults.
Subacute onset of progressive cognitive deficits, behavioural problems, spasticity, rigidity,
Myoclonus, generalised seizures
Findings on Investigations:
EEG: flat with episodic bursts
Anti-measles antibodies
CSF: raised IgG index
Pathology:
Gross: hard brain (gliosis), Microscopic: intracellular (type A) and intracytoplasmic neuronal and glial inclusions