Synonyms:
Malignant atrophic papulosis
Diagnosis:
Clinical:
- Skin, brain & bowel vasculitis
- Skin: initially red papules then, umbilicated papules, +white centre & telangiectatic rim
- Bowel: GI bleed, bowel perforation
MRI:
- Infarcts
- T2 hyperintensities, +small hemorrhagic areas
- T1 +GAD: dural enhancement may occur
Cather Angiogram/angiography:
- Vasculitis features
- Peripheral aneurysms
- Also stenosis in GI arteries e.g. coeliac artery