Chilhood Epilepsy Syndromes

For each syndrome seizure disorder a combination of history, physical examination & EEG are used
Childhood absence epilepsy CAE
Juvenile absence epilepsy JAE
West syndrome a.k.a. Infantile spasms
Aicardi syndrome a.k.a. Aicardi-Goutieres syndrome
Jeavons Syndrome (Eyelid myoclonia with or without absences)
Lennox-Gestuat syndrome
Benign epilepsy with centrotemporal spikes BECTS a.k.a. benign rolandic epilepsy
Juvenile myoclonic epilepsy JME a.k.a. Janz syndrome
Idiopathic generalized epilepsy with Generalized tonic-clonic seizures only
Focal epilepsy (cryptogenic, symptomatic)
Severe myoclonic epilepsy of infancy (SMEI) a.k.a. Dravet’s syndrome
Epilepsy with Continuous spike-waves in slow sleep
Benign epilepsy with occipital paroxysms
Landau-Kleffner syndrome LKS
Myoclonic astatic epilepsy of childhood
Ohtahara syndrome
Early myoclonic encephalopathy
Benign myclonic epilepsy in infancy
Early onset benign childhood occipital epilepsy a.k.a. Early onset benign childhood seizures with Occipital spikes a.k.a. Panayiotopoulos syndrome
Late onset childhood occipital epilepsy (Gestaut type)
Epilepsy with myoclonic absences
Myoclonic-astatic epilepsy of childhood a.k.a. Epilepsy with myoclonic astatic seizures
Idiopathic photosensitive occipital lobe epilepsy
Primary reading epilepsy
Startle epilepsy
Benign familial neonatal seizures a.k.a. Benign Familial neonatal convulsions (benign infantile epilepsy)
Autosomal dominant nocturnal frontal lobe epilepsy (ADNFLE)
Generalised epilepsy with febrile seizures plus (GEFS+)
Autosomal dominant partial epilepsy with auditory features a.k.a. Autosomal dominant lateral temporal epilepsy (ADTLE)

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