Synonyms:
a.k.a. anti-chondroitin sulfate neuropathy:
Diagnosis:
The diagnosis is made based on clinical features supported by electrodiagnostic tests and antibodies
Clinical features:
Polyneuropathy (sensory, or sensorimotor, sensory>motor), ataxia may occur,
Findings on investigations:
Anti-sulfatide antibody (a.k.a. anti-chondroitin sulfate): positive, > 1:1000 titre
SPEP +IFE: usually have monoclonal IgM
NCS/EMG:
- Mainly demyelinating pattern with secondary axonal loss